Akademik Veri Yönetim Sistemi
XVIII ECDMER European Congress of DentoMaxilloFacial Radiology, Lublin, Polonya, 8 - 10 Haziran 2022, ss.77
Objective: Sagliker Syndrome is a rare form of renal osteodystrophy resulted from untreated secondary
hyperparathyroidism. It is described as high levels of parathyroid hormones in patients with chronic renal failure,
maxillary and mandibular deformities, dental abnormalities and various kinds of skeletal changes including short stature
and fingertip abnormalities. In this case report it is aimed to present the clinical and radiological features of a patient with
the former mentioned characteristics.
Case Report: A 20-year-old male patient has been suffering from chronic kidney disease applied to our clinic with the
complaints of slowly progressing painless swelling of his jaw for the past 6 months. Extraoral examination revealed
walking disability, fingertip deformities, swelling in the maxilla and mandible. Intraoral examination revealed hard
swelling in the palatal bone and mandible, difficulty in closing the mouth and mobility in the teeth. In the panoramic and
cone beam computed tomography images; ground glass appearance in the maxillary and mandibular bones,
polydiastema, lamina dura loss in the teeth and enlargement of the cranium and viscerocranium bones in the field of
view were observed. The biochemical and radiologic features were compatible with Sagliker Syndrome. The patient was
consulted to a nephrologist tor total parathyroidectomy.
Conclusion: In addition to the unique radiological and clinical features, high levels of alkaline phosphatase and parathyroid hormones should encourage the clinicians to search for syndrome-like diseases,such as Sagliker Syndrome
and and a multidisciplinary approach should be carried out.