Pediatric Tonsillar Synovial Sarcoma-Very Rare Localization: A Case Report and Review of the Literature

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Yalcin K., Tuysuz G., GENÇ M., ÖZBUDAK İ. H., DERİN A. T., KARAALİ K., ...Daha Fazla

TURKISH JOURNAL OF PATHOLOGY, cilt.36, sa.1, ss.82-86, 2020 (ESCI) identifier identifier identifier

  • Yayın Türü: Makale / Derleme
  • Cilt numarası: 36 Sayı: 1
  • Basım Tarihi: 2020
  • Doi Numarası: 10.5146/tjpath.2018.01449
  • Dergi Adı: TURKISH JOURNAL OF PATHOLOGY
  • Derginin Tarandığı İndeksler: Emerging Sources Citation Index (ESCI), Scopus, Academic Search Premier, EMBASE, MEDLINE, Directory of Open Access Journals, TR DİZİN (ULAKBİM)
  • Sayfa Sayıları: ss.82-86
  • Anahtar Kelimeler: Synovial Sarcoma, Tonsillar neoplasm, Pediatric tumor, Dysphagia, Snoring, SOFT-TISSUE SARCOMAS, PROGNOSTIC-FACTORS, HEAD, NECK, ADOLESCENTS, SURVIVAL, MULTICENTER, ONCOLOGY, CHILDREN, TRIAL
  • Akdeniz Üniversitesi Adresli: Evet

Özet

Tonsillar synovial sarcoma is an extremely rare entity and only 9 adult patients have been reported up to now. Here, we describe the first pediatric tonsillar synovial sarcoma of the literature in a patient who presented with a 2-month history of dysphagia and snoring. Clinical and radiological examinations showed that the tumor arose from the right palatine tonsil and narrowed the parapharyngeal space. An incisional biopsy from the palatine tonsil revealed the diagnosis of synovial sarcoma. The patient has underwent total tonsillectomy and received radiotherapy and chemotherapy because of the positive surgical margins. The patient is clinically in good condition and free of tumor 30 months after the initial diagnosis. We achieved a long-term complete remission with a combination of surgery, radiotherapy and chemotherapy in our case. Tonsillar synovial sarcoma should be kept in mind while dealing with tonsillar masses. We can conclude that a multidisciplinary approach is warranted while treating synovial sarcoma with this localization.